[1] Primary erythroderma arises on normal looking skin due to an underlying systemic disorder including malignancy or because of a drug reaction, while secondary erythroderma arises from pre-existing dermatoses like psoriasis, atopic dermatitis,
Pityriasis rubra pilaris and actinic dermatosis.
Among all, 112 pieces of data were psoriasis, 61 seboreic dermatitis, 72 lichen planus, 49 pityriasis rosea, 52 cronic dermatitis and 20
pityriasis rubra pilaris. It was also discovered that the database contains 34 attributes, 33 of which were linear valued and one of them was nominal.
An association between HS and several other inflammatory and genetic disorders have also been reported in the literature, including acne conglobata, spondyloarthropathies, pyoderma gangrenosum, synovitis-acne-pustulosis-hyperostosis-osteitis syndrome, Dowling-Degos disease, fox den disease, florid steatocystoma multiplex, pyoderma vegetans, and
pityriasis rubra pilaris (6-14).
Erythemato-squamous diseases to be classified include
pityriasis rubra pilaris, seborrheic dermatitis, psoriasis, lichen planus, chronic dermatitis, and pityriasis rosea.
The differential diagnosis for erythroderma includes psoriasis, drug reaction, atopic dermatitis (AD),
pityriasis rubra pilaris, and CTCL, with AD, drug eruption, and psoriasis being most common.
Choate cited other recent developments, including the discovery that familial
pityriasis rubra pilaris is caused by mutations in CARD 14, which is a known activator of nuclear factor kappa B signaling (Am J Hum Genet.
The patient was given a diagnosis of
pityriasis rubra pilaris (PRP) based on her distinctive clinical presentation.
While CTCL is the biggie in the differential diagnosis of very-late-onset atopic dermatitis, other conditions that need to be considered include psoriasis, contact dermatitis,
pityriasis rubra pilaris, and pityriasis rosea.
Other dermatological conditions which may give rise to hyperkeratosis include lichen planus and
pityriasis rubra pilaris. The former is characterised by itchy, purple, flat topped papules around the ankles and wrists of adults.
In particular lymphoma; hereditary disorders (ichthyosis,
pityriasis rubra pilaris); various types of eczema, pemphigus, lichen planus, dermatophytosis, scabies, and dermatomyositis; and autoimmune diseases in general usually offer characteristic histopathologic findings.