Summary of 10 Previously Reported Patients With Pulmonary Crystal-Storing Histiocytosis
(CSH) Solitary or Multiple Maximum Nodules Nodule Source, y y/Sex (No.
Intrahepatic causes of portal hypertension included: biliary atresia (20); congenital hepatic fibrosis syndromes (3); neonatal hepatitis (1); auto-immune hepatitis (1); Alagille syndrome (1); Langerhans cell histiocytosis
(1); and idiopathic cirrhosis (3).
Malignant diseases associated with EAC include myelomatosis, Hodgkin's lymphoma, acute leukemia, prostatic adenocarcinoma, nasopharyngeal carcinoma and histiocytosis
2 Systemic disorders: sarcoidosis, pulmonary Langerhans cell histiocytosis
, lymphangioleiomyomatosis, neurofibromatosis, vasculitis
Andrew, 14, has Langerhans' Cell Histiocytosis
Armani Wainwright, of Milnsbridge, suffers from Langerhans cell histiocytosis
- a rare condition which demonstrates the same symptoms as cancer.
Histological evaluation demonstrated granulation tissue with focal necrosis and dystrophic calcification, multinucleated giant cells, old hemorrhagic products, reactive histiocytosis
at the periphery, and rare black angulated metallic fragments (Fig.
Many systemic diseases are associated with advanced alveolar bone loss that may lead to premature loss of teeth, such as hypophosphatesia, Papillon-Lefevre syndrome, histiocytosis
X, agranulocytosis, leukocyte adherence deficiency, neutropenias, leukemias, diabetes mellitus, scleroderma, fibrous dysplasia, acrodynia, and Chediak-Higashi syndrome [Armitage, 1999].
was present in 3 of 3 spleens examined from birds in group 1 (azithromycin) (3 marked, 1 spleen not found at necropsy, 2 spleens had insufficient tissue for both histopathology and PCR); 7 of 7 spleens from group 2 (21-day doxycycline) (5 marked, 2 moderate); 4 of 6 spleens from group 3 (45-day doxycycline) (3 marked, 1 moderate, 2 insufficient tissue for histopathology and PCR); and 3 of 4 spleens from group 4 (control) (3 marked, 1 not found at necropsy).
The differential diagnosis of granulomas in the GI tract includes mycobacterium, syphilis, histoplasma infection, gastric cancer and lymphoma, Langerhans cell histiocytosis
, as well as Crohn and Whipple diseases.
Mrs Hattersley was diagnosed with histiocytosis
X when she was 19, which means she will never be able to undergo a general anaesthetic or do anything that puts a strain on her heart or lungs.
Sharmin Ahmed, five, suffers from Langerhans Cell Histiocytosis
(LCH), which affects just one in 200,000 people.