PPPK can be associated with Darier's
disease and Cowden disease.
sign is not always demonstrable, especially in those with a long history of the disorder and is not 100% specific for mastocytosis, since it has also been described rarely in juvenile xanthogranuloma and acute lymphoblastic leukemia of neonates.
sign (the development of a hive or wheal when a lesion is stroked) was present.
In the second category we find chronic dermatological diseases, such as: psoriasis, acne excoriee, alopecia, atopic dermatitis, chronic forms of urticaria, endogenous eczema, prurigo nodularis, Darier's
disease, lichen simplex chronicus, recidivant herpes simplex infection etc.
Warty dyskeratoderma is an uncommon solitary lesion occurring in skin or oral mucosa which has histopathological similarity to Darier's
disease and hence is referred to as isolated Darier's
3 It occurs with various skin diseases, such as atopic dermatitis, Wiskott- Aldrich syndrome, pemphigus foliaceus, ichthyosis vulgaris, bullous pemphigoid, seborrheic dermatitis, psoriasis, irritant contact dermatitis and Darier's
Prior studies have found that AI patients had a lower quality of life than did patients with other chronic skin diseases such as acne vulgaris, psoriasis, atopic dermatitis, alopecia, Darier's
disease, and morbus Hailey-Hailey, the researchers noted.
disease is a rare autosomal dominant genodermatosis characterised by warty papules and plaques in the seborrhoeic regions, palmoplanar pits, and distinctive nail dystrophy.
Desmosomal dissolution in Grover's disease, Hailey-Hailey's disease and Darier's
Diagnosed with Darier's
Disease at the age of 21, the condition causes painful hard blisters to break out all over her body and also causes her nails to split.
Munro CS: The phenotype of Darier's
disease: penetrance and expressivity in adults and children.
Mast cell tumors that degranulate, causing a local erythema and wheal formation when manipulated, are referred to as having a positive Darier's