Gorlin syndrome

(redirected from Nevoid basal cell carcinoma syndrome)
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Related to Nevoid basal cell carcinoma syndrome: Gorlin Syndrome, ameloblastoma, Basal Cell Nevus Syndrome, Calcifying odontogenic cyst

Gorlin syndrome

(ˈɡɔːlɪn)
n
1. (Pathology) a rare congenital disorder in which cancer destroys the facial skin and causes blindness; skeletal anomalies and some mental retardation can also occur
2. (Medicine) a rare congenital disorder in which cancer destroys the facial skin and causes blindness; skeletal anomalies and some mental retardation can also occur
[C20: named after R. J. Gorlin (1923–2006), US oral pathologist]
References in periodicals archive ?
None of the keratocystic odontogenic tumors was associated with nevoid basal cell carcinoma syndrome.
Key words: Odontogenic keratocyst (OKC), Keratocystic odontogenic tumor (KCOT), Nevoid basal cell carcinoma syndrome (NBCCS).
Early diagnosis of Nevoid basal cell carcinoma syndrome.
Nevoid basal cell carcinoma syndrome (NBCCS), also known as basal cell nevus syndrome, multiple basal cell carcinoma syndrome, Gorlin syndrome, and Gorlin-Goltz syndrome, is an inherited medical condition involving defects within multiple body systems such as the skin, nervous system, eyes, endocrine system, and bones.
Basal cell nevus syndrome or nevoid basal cell carcinoma syndrome (BCNS; Gorlin syndrome) is a rare autosomal, dominantly inherited condition with variable expressivity, although 30% to 50% of cases are due to spontaneous mutations.