A rare AV malformation may arise from a persisting fistulous connection of choroidal arteries when the median prosencephalic
vein which does not regress normally could serve as another path for air emboli to enter the arterial circulation, though true incidence of vein of Galen malformation is reported at <1% .
 Central Nervous System (CNS) abnormalities associated with MKS include Dandy-Walker malformation, agenesis of the corpus callosum, microcephaly, rhombic roof dysgenesis and prosencephalic
Fetal cerebral malformation, predominantly of impaired prosencephalic
development namely agenesis of the corpus callosum and septo-optic dysplasia, is the main pathological feature in fetus, and causes prominent neurodevelopmental retardation, and associated with congenital facial anomalies and visual disorders [1-3].