(9) Adicionalmente el consumo de carnes de animales que padecen la encefalopatia espongiforme bovina (EEB) ha sido relacionada con la aparicion de casos atipicos en adultos jovenes humanos (nvCJD
) reconocidos en el Reino Unido y Francia; un modelo en ratones llevado a cabo por Bruce y colaboradores demuestra que la nvCJD
es causada por el mismo agente de la EEB, sus caracteristicas la hacen diferente de la forma esporadica aunque las propiedades de la transmision podrian tambien relacionarse con ciertos factores geneticos del huesped que controlan el tiempo de progresion de la enfermedad.
New variant CJD (nvCJD
) was first identified in 1996 and affects mostly younger adults (average age 27)
"The Foods Standards Agency has said that the return of beef from older cattle which have tested negative for BSE presents a less than three per cent chance of triggering an nvCJD
case every 60 years," said NBA chairman, Robert Robinson.
Only one case of nvCJD
has been reported in the United States, and that was an person in Florida who recently had moved from the United Kingdom, Nixon said.
But dentists and other health service professionals are mistakenly taking the guidance to include nvCJD
families, as well as inherited CJD families.
The head of an expert panel of the Health, Labor and Welfare Ministry expressed his view Thursday that a teenage girl in a Tokyo area hospital does not have new variant Creutzfeldt-Jakob disease (nvCJD
), a fatal brain-wasting illness linked to mad cow disease, as earlier suspected.
(126.) Paul Brown et al., Bovine Spongiform Encephalopathy and Variant Creutzfeldt-Jakob Disease: Background, Evolution, and Current Concerns, 7 EMERGING INFECTIOUS DISEASE 6, 11 (2001) (Two cases of vCJD were confirmed in France and one case was confirmed in the Republic of Ireland.); see also Tan et al., supra note 123, at 2335 ("Although WHO and the EU state that transmission of CJD via blood cannot currently be confirmed and too few data on nvCJD
exist to make recommendations, they advocate exclusion of blood donation by people who have or are at risk for CJD.").
However, new variant CJD (appropriately called nvCJD
) has taken the lives of almost 100 people in the U.K, Ireland, and France, and has been linked to BSE, most probably because CJD victims consumed products that contained brain or spinal cord tissue from BSE-infected cattle prior to exhibiting symptoms of BSE.
In England, BSE is linked with a new variant of CJD in humans, known as NVCJD
An expert panel of the Health, Labor and Welfare Ministry said Thursday the possibility is low that a teenage girl in a Tokyo area hospital has new variant Creutzfeldt-Jakob disease (nvCJD
), a fatal brain-wasting illness linked to mad cow disease, as earlier feared.
And what was identified as new variant Creutzfeld-Jakob Disease (nvCJD
) after the emergence of BSE in the 1980s is probably not a new disease, it has been claimed.
Recently, a novel form of human prion disease (nvCJD
) that is thought to be linked with bovine spongiform encephalopathy has been described.